Overview

Definition:
-Pediatric Acute Respiratory Distress Syndrome (ARDS) is a life-threatening condition characterized by diffuse lung inflammation and acute respiratory failure
-It is defined by the presence of acute onset hypoxemia (PaO2/FiO2 ratio < 300 mmHg, or in infants, lower thresholds based on age and lung injury), bilateral pulmonary infiltrates on chest imaging consistent with edema, and a non-cardiogenic cause of pulmonary edema.
Epidemiology:
-The incidence of pediatric ARDS varies significantly by study and definition used, ranging from 1 to 4 per 100,000 children annually
-Sepsis and pneumonia are the most common underlying causes in children, unlike in adults where pneumonia is also primary but other causes like aspiration are more prevalent
-Mortality rates remain high, around 20-40%, though improvements in supportive care, including lung-protective ventilation and judicious fluid management, have led to some decline.
Clinical Significance:
-Pediatric ARDS is a critical medical emergency requiring prompt recognition and management
-Inadequate or excessive fluid administration can exacerbate lung injury, leading to worsening hypoxemia, prolonged mechanical ventilation, increased risk of nosocomial infections, and greater mortality
-Understanding current evidence-based fluid management strategies is paramount for pediatric residents and specialists preparing for DNB and NEET SS examinations.

Clinical Presentation

Symptoms:
-Sudden onset of severe dyspnea
-Rapid breathing (tachypnea)
-Increased work of breathing, including nasal flaring, retractions, and grunting
-Cough, often non-productive initially
-Cyanosis or pallor
-Lethargy or decreased level of consciousness.
Signs:
-Tachycardia
-Hypotension or hypertension depending on underlying cause and shock status
-Auscultation reveals diffuse crackles or diminished breath sounds
-Chest X-ray shows bilateral opacities not fully explained by lobar collapse or consolidation
-Arterial blood gas (ABG) demonstrating severe hypoxemia refractory to supplemental oxygen.
Diagnostic Criteria:
-The Berlin Definition for ARDS is adapted for pediatrics
-Key components include: 1
-Acute onset (within 1 week of a clinical insult or new/worsening respiratory symptoms)
-2
-Respiratory failure not fully explained by cardiac factors or fluid overload
-3
-Bilateral opacities on chest imaging (X-ray or CT) not fully explained by effusions, lobar/lung collapse, or nodules
-4
-Severe hypoxemia: PaO2/FiO2 ratio < 300 mmHg
-For infants, modified criteria may use lower thresholds, and oxygenation targets are age-adjusted.

Diagnostic Approach

History Taking:
-Focus on the precipitating event: recent infection (pneumonia, sepsis), aspiration (vomiting, foreign body), trauma, near-drowning, or underlying comorbidities (immunodeficiency, congenital heart disease, neuromuscular disorders)
-Timeline of symptom onset is crucial
-History of fluid intake and output, and signs of cardiac dysfunction.
Physical Examination:
-Comprehensive assessment of respiratory effort: respiratory rate, use of accessory muscles, grunting, nasal flaring
-Palpate for chest wall tenderness
-Auscultate for breath sounds, crackles, wheezes, and murmurs
-Assess for peripheral edema and jugular venous distension to evaluate for fluid overload
-Assess for signs of sepsis or shock.
Investigations:
-Arterial blood gas (ABG) for oxygenation and ventilation assessment (PaO2, PaCO2, pH)
-Complete blood count (CBC) to assess for infection
-Blood cultures if sepsis is suspected
-Chest X-ray or CT scan to identify infiltrates and rule out other causes
-Echocardiography to assess cardiac function and rule out cardiogenic pulmonary edema
-Inflammatory markers (CRP, procalcitonin)
-Coagulation profile if disseminated intravascular coagulation (DIC) is suspected
-Sputum Gram stain and culture if pneumonia is present
-Toxicology screen if aspiration is suspected.
Differential Diagnosis:
-Cardiogenic pulmonary edema (secondary to congenital heart disease, myocarditis)
-Pulmonary hemorrhage
-Diffuse pneumonia (bacterial, viral, fungal)
-Pulmonary embolism
-Acute lung injury from trauma or inhalation
-Near-drowning
-Acute exacerbations of chronic lung diseases (e.g., cystic fibrosis)
-Congenital pulmonary airway malformations.

Management

Initial Management:
-Immediate stabilization is critical
-Optimize oxygenation with highest possible FiO2
-Initiate mechanical ventilation
-Secure airway and establish IV access
-Treat underlying cause (e.g., antibiotics for pneumonia/sepsis).
Medical Management:
-Lung-protective ventilation strategies: low tidal volumes (4-6 mL/kg ideal body weight), appropriate PEEP to maintain alveolar recruitment, and permissive hypercapnia
-Sedation and analgesia
-Neuromuscular blockade judiciously if severe ventilator dyssynchrony persists
-Bronchodilators if bronchospasm is present.
Fluid Management Strategies:
-The cornerstone of pediatric ARDS fluid management is a conservative or restricted fluid strategy
-Aim for a negative or neutral fluid balance
-Frequent assessment of fluid status: daily weights, intake/output charting, urine output, and assessment for peripheral edema
-Consider diuretics (e.g., furosemide) if signs of fluid overload are evident and respiratory mechanics are compromised
-Avoid fluid boluses unless hemodynamic compromise is present and not attributable to ARDS
-Monitor central venous pressure (CVP) and cardiac output (if available) cautiously
-Echocardiography can be invaluable in assessing fluid responsiveness.
Supportive Care:
-Nutritional support: early enteral nutrition is preferred to minimize gut atrophy and translocation of bacteria
-Consider parenteral nutrition if enteral is not feasible
-Glycemic control
-Prevention of ventilator-associated pneumonia (VAP) and other healthcare-associated infections
-DVT prophylaxis (mechanical or pharmacologic depending on risk)
-Prone positioning can improve oxygenation in moderate to severe ARDS
-Consider extracorporeal membrane oxygenation (ECMO) for severe refractory hypoxemia despite maximal conventional management.

Complications

Early Complications:
-Worsening hypoxemia and respiratory failure
-Barotrauma and volutrauma from mechanical ventilation
-Pneumothorax
-Ventilator-associated pneumonia (VAP).
Late Complications:
-Pulmonary fibrosis and long-term lung dysfunction (bronchopulmonary dysplasia)
-Neurological sequelae (e.g., developmental delay)
-Muscle weakness and deconditioning
-Post-intensive care syndrome (PICS).
Prevention Strategies:
-Adherence to lung-protective ventilation strategies
-Judicious fluid management to prevent overload
-Early initiation of enteral nutrition
-Strict infection control protocols
-Prompt treatment of underlying causes
-Minimizing sedation and early mobilization where possible.

Prognosis

Factors Affecting Prognosis:
-Severity of ARDS (oxygenation index)
-Age of the child (infants may have worse outcomes)
-Presence of comorbidities
-Underlying cause of ARDS (sepsis and trauma generally associated with higher mortality)
-Duration of mechanical ventilation and ICU stay
-Development of complications like VAP or multi-organ dysfunction syndrome (MODS).
Outcomes:
-Survival rates for pediatric ARDS have improved but remain significant
-Survivors may experience short-term sequelae such as reduced lung function and exercise intolerance
-Some children may develop long-term respiratory morbidity and neurodevelopmental deficits
-Early and aggressive management, including appropriate fluid management, is crucial for improving outcomes.
Follow Up:
-Children recovering from ARDS require comprehensive follow-up
-This includes regular assessment of pulmonary function, growth and development monitoring, and rehabilitation services if needed
-A multidisciplinary approach involving pulmonologists, physical therapists, and developmental specialists is often beneficial
-Neurodevelopmental assessment should be a routine part of follow-up for infants and young children.

Key Points

Exam Focus:
-Conservative fluid management is key in pediatric ARDS to prevent worsening pulmonary edema
-Recognize pediatric ARDS using adapted Berlin criteria
-Lung-protective ventilation strategies (low tidal volumes, PEEP) are mandatory
-Consider ECMO for refractory hypoxemia
-Understand common triggers: sepsis, pneumonia, aspiration.
Clinical Pearls:
-Think fluid restriction FIRST in pediatric ARDS unless clear evidence of hypovolemia or shock
-Daily weights are your friend
-Echocardiography is invaluable for fluid assessment
-Prone positioning can significantly improve oxygenation
-Treat the underlying cause aggressively
-Long-term follow-up is essential for survivors.
Common Mistakes:
-Over-resuscitation with fluids leading to pulmonary edema and worsening ARDS
-Aggressive fluid management in the absence of clear hypovolemia
-Inadequate PEEP leading to alveolar collapse
-Using high tidal volumes which can cause ventilator-induced lung injury
-Neglecting nutritional support
-Failure to identify and treat the underlying precipitating cause promptly.