Overview

Definition:
-Gynecomastia refers to the enlargement of male breast tissue
-In pediatrics, it is crucial to distinguish between true gynecomastia (glandular proliferation) and pseudogynecomastia (adipose tissue accumulation, often associated with obesity).
Epidemiology:
-Physiologic gynecomastia occurs in approximately 60-90% of adolescent males during puberty due to transient hormonal imbalances
-True pathologic gynecomastia is less common
-Obesity is a significant contributor to pseudogynecomastia, affecting a large proportion of overweight or obese children and adolescents.
Clinical Significance: Accurate differentiation is vital to avoid unnecessary investigations and interventions for benign conditions like obesity-related pseudogynecomastia, while ensuring timely diagnosis and management of underlying pathologic causes of true gynecomastia, which can indicate serious endocrine or neoplastic conditions.

Clinical Presentation

Symptoms:
-May be asymptomatic
-Tenderness or pain in the breast tissue
-Palpable rubbery or firm disc beneath the nipple-areola complex
-Rapid onset of breast enlargement
-History of medications or exposures
-Symptoms suggestive of underlying endocrine disorder, such as delayed puberty or other signs of virilization or feminization.
Signs:
-Bilateral or unilateral breast enlargement
-Palpation reveals glandular tissue (firm, mobile disc) or adipose tissue (softer, diffuse)
-Absence of nipple discharge
-Absence of palpable masses in the breast parenchyma or axilla
-Associated signs of obesity, such as increased BMI, or signs of specific endocrine disorders (e.g., hypospadias, cryptorchidism, ambiguous genitalia).
Diagnostic Criteria:
-No universal diagnostic criteria exist for pediatric gynecomastia
-Diagnosis relies on clinical examination distinguishing glandular tissue from adipose tissue
-Elevated estrogen or depressed testosterone levels may support hormonal imbalance
-Genetic testing may be indicated for suspected disorders of sex development.

Diagnostic Approach

History Taking:
-Detailed birth and developmental history
-Pubertal status (Tanner staging)
-Family history of endocrine disorders or breast cancer
-Detailed medication history, including over-the-counter drugs, herbal supplements, and recreational drug use
-History of liver disease, renal disease, hyperthyroidism, or chronic illness
-Exposure to endocrine disruptors
-Presence of symptoms like testicular pain or changes, galactorrhea, or constitutional symptoms.
Physical Examination:
-Comprehensive assessment of pubertal development (Tanner staging for genitalia and pubic hair)
-Careful palpation of breast tissue to differentiate between glandular and adipose tissue
-Measurement of testicular volume
-Examination for other signs of endocrine dysfunction: thyroid, adrenal, or signs of Klinefelter syndrome (e.g., tall stature, eunuchoid habitus, small testes)
-Assessment of body mass index (BMI) and distribution of adipose tissue.
Investigations:
-Initial investigations are guided by clinical suspicion
-For suspected true gynecomastia: Serum hormone levels including total testosterone, luteinizing hormone (LH), follicle-stimulating hormone (FSH), prolactin, estradiol, and dehydroepiandrosterone sulfate (DHEAS)
-Consider human chorionic gonadotropin (hCG) if Leydig cell tumor is suspected
-Thyroid function tests (TSH, free T4) if hyperthyroidism is suspected
-Karyotype if Klinefelter syndrome or disorders of sex development are suspected
-Liver and renal function tests if systemic disease is suspected
-Imaging is generally not required for simple obesity-related pseudogynecomastia
-Ultrasound may be useful to assess breast tissue composition if differentiation is unclear
-Testicular ultrasound may be indicated if a testicular tumor is suspected.
Differential Diagnosis:
-Obesity-related pseudogynecomastia (most common)
-True gynecomastia due to pubertal delay or imbalance
-Klinefelter syndrome (47,XXY)
-Testicular tumors (Leydig cell tumors, seminomas)
-Adrenal tumors (producing androgens or estrogens)
-Medications (e.g., spironolactone, cimetidine, anabolic steroids, digoxin)
-Liver disease
-Hyperthyroidism
-Hypogonadism
-Certain rare genetic syndromes
-Gynecomastia due to estrogen-producing tumors (rare in children).

Management

Initial Management:
-For obesity-related pseudogynecomastia: Lifestyle modification is paramount
-Focus on weight loss through diet and exercise
-Reassurance is key
-For pubertal gynecomastia: Reassurance and observation are usually sufficient as it often resolves spontaneously within 1-3 years
-Monitor pubertal progression and hormonal status.
Medical Management:
-Pharmacologic treatment is generally reserved for persistent, symptomatic true gynecomastia after puberty or in specific pathologic conditions
-Options include aromatase inhibitors (e.g., anastrozole, letrozole) or selective estrogen receptor modulators (SERMs, e.g., tamoxifen)
-Dosing and duration require expert consultation and are typically not indicated in the pediatric age group for benign pubertal gynecomastia.
Surgical Management:
-Surgical intervention (e.g., mastectomy, liposuction) is typically considered for persistent, bothersome true gynecomastia after puberty, or if significant cosmetic deformity exists
-Indications and timing are carefully evaluated by a pediatric surgeon and endocrinologist
-It is rarely indicated in prepubertal or early pubertal boys.
Supportive Care:
-Psychological support is crucial for affected adolescents, addressing body image concerns and potential bullying
-Education of parents and child about the condition and its typical course
-Regular follow-up to monitor pubertal development and symptom resolution
-Management of any underlying systemic disease.

Complications

Early Complications:
-Psychological distress, anxiety, and depression related to body image concerns
-Pain and tenderness associated with breast tissue enlargement
-Early complications are rare for benign causes.
Late Complications:
-Persistent gynecomastia leading to long-term cosmetic concerns and psychological impact
-In rare cases of malignancy, delayed diagnosis can lead to poorer prognosis
-If associated with underlying genetic conditions, other organ system involvement may occur.
Prevention Strategies:
-Primary prevention focuses on maintaining a healthy weight in childhood to reduce the incidence of obesity-related pseudogynecomastia
-Avoiding exposure to known endocrine disruptors and unnecessary medications
-Early diagnosis and management of endocrine disorders are crucial.

Prognosis

Factors Affecting Prognosis:
-The underlying cause is the most significant factor
-Obesity-related pseudogynecomastia and benign pubertal gynecomastia have an excellent prognosis with spontaneous resolution or weight management
-True gynecomastia due to malignancy or severe endocrine disorders carries a prognosis dependent on the primary condition.
Outcomes:
-Most cases of adolescent gynecomastia and pseudogynecomastia resolve spontaneously with time and weight loss
-Persistent cases may benefit from medical or surgical intervention
-Prognosis for malignancy-associated gynecomastia depends on the specific cancer.
Follow Up:
-Regular follow-up with a pediatrician or pediatric endocrinologist is recommended, particularly for true gynecomastia, to monitor for resolution, progression, or development of complications
-For obesity-related pseudogynecomastia, follow-up focuses on weight management and overall health.

Key Points

Exam Focus:
-Differentiating pseudogynecomastia (fat) from true gynecomastia (glandular tissue) on palpation is a key clinical skill
-Understand the hormonal milieu of puberty and common endocrine causes of true gynecomastia (e.g., Klinefelter, Leydig cell tumors)
-Recognize medications that cause gynecomastia.
Clinical Pearls:
-Always start with a thorough history and physical examination, including Tanner staging and testicular volume measurement
-Reassurance is paramount for benign conditions
-Never dismiss unexplained gynecomastia without appropriate hormonal workup, especially if pubertal development is abnormal or other systemic symptoms are present.
Common Mistakes:
-Over-investigating obesity-related pseudogynecomastia
-Under-investigating true gynecomastia, particularly in the presence of other signs of endocrine dysfunction
-Delaying referral to endocrinology or surgery when indicated
-Incorrectly attributing all breast enlargement in obese boys to simple fat accumulation without considering glandular pathology.